Scimitar Syndrome

Video Supplement to "Scimitar Syndrome" (Clinical Image).

Video 1. Mediastinal shift to the right, secondary to right lung hypoplasia is noted. Right pulmonary artery (RPA) angiogram in posteroanterior and lateral views shows the RPA with a bilobar branching pattern. Levophase shows anomalous pulmonary venous drainage of the right pulmonary veins (PAPVC) into a vertical vein that drains into the inferior vena cava, classically described as a “Scimitar” vein due to its resemblance in appearance to the Turkish sword. 3D reconstructed image shows the PAPVC (in purple) and aortopulmonary collaterals (APCs) from the aorta supplying the right lungs (in red). Two prominent APCs supplying the right lung were noted—one from the descending thoracic aorta (DTA) and one from the celiac artery—along with 2 minor APCs from the DTA. The APCs are seen on the digital substraction angiography as well.

Video 2: Procedure video of transcatheter aortopulmonary collateral device closure. The aortopulmonary collateral (APC) was hooked and selective angiograms were taken. Sizes of the APC were reconfirmed and closure was done with Amplatzer Vascular Plug II devices (Abbott). Post-deployment angiogram showed good position.